L-Phenylalanine CAS: 63-91-2 99% Phofo e tšoeu
| Nomoro ea lethathamo | XD90317 |
| Lebitso la Sehlahiswa | L-Cysteine hydrochloride anhydrous |
| CAS | 63-91-2 |
| Foromo ea limolek'hule | C9H11NO2 |
| Boima ba Molek'hule | 165.19 |
| Lintlha tsa polokelo | Ambient |
| Khoutu ea Lekhetho e Kopantsoeng | 29224985 |
Tlhaloso ea Sehlahisoa
| Ponahalo | Phofo e tšoeu ea kristale |
| Tlhahlobo | 99% |
| Ho potoloha ho itseng | -20,4 ho ea ho -35,2 |
| Litšepe tse boima | <0.002% |
| Ketapele | <10mg/kg |
| pH | 5.4 - 6 |
| Tahlehelo ka ho Omisa | <0.40% |
| Masalla a ho Ignition | <0.10% |
Ho lefu la moroto oa sirapo ea maple (MSUD), branched-chain L-amino (BCAA) le 2-oxo acids (BCOA) li bokellana ka marong a 'mele ka lebaka la khaello e futsitsoeng ea tšebetso e rarahaneng ea branched-chain 2-oxo acid dehydrogenase.Ho MSUD, ho na le tlhahisoleseling e nyane mabapi le bohlokoa ba ho lahla moroto oa metsoako ea ketane ea makala.Re ile ra hlahloba ho hlakoloa ha renal ea leucine, valine, isoleucine le alloisoleucine, le 2-oxo acids 4-methyl-2-oxopentanoate (KIC), 3-methyl-2-oxobutanoate (KIV), (S) - (S-) KMV), le (R) -3-methyl-2-oxopentanoate (R-KMV), ho sebelisa lipara tsa plasma le moroto (n = 63) ho tsoa ho bakuli ba 10 ba nang le MSUD ea khale.Ho ntšoa ha renal ha BCAA ea mahala ho ne ho le maemong a tloaelehileng (<0.5%) mme e sa ipapise le khatello ea mali ea plasma.Ho ntšoa ha BCAA e tlanngoeng (N-acylated) e ne e tloaelehile ebile e sa itšetlehe haholo ka likhakanyo tsa plasma tsa BCAA.Ho ntšoa ha renal ka karoloana ea BCOA e ne e le ka tatellano ea KIC << KIV
